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Abstract. Neonatal hemochromatosis is a rare congenital disorder which
affects both fetuses and newborns. It is characterized by hepatocellular
failure, often appearing on the first day of life in the form of coagulopathy,
hypoalbuminemia, hypoglycemia, and jaundice. Most of the affected infants die
early in life, and definitive diagnosis has often been made only by post-mortem
evaluation. With the help of MRI, plus increasing awareness of the disorder,
diagnosis is now often made early, even in utero. Duplex Doppler sonography does
not provide information on siderosis but shows abnormalities in the liver or
blood-flow patterns associated with liver disease.